Short QT syndrome is a rare and genetically heterogeneous disorder characterized by a short QT interval (QT <340 ms or QTc <350 ms). It is inherited in an autosomal dominant pattern. Patients can present with atrial and ventricular arrhythmias (including atrial fibrillation, polymorphic VT, and VF) and syncope. Patients with short QT syndrome are considered to be at very high risk for SCD; therefore, ICD placement is recommended in all patients.